A

ABCB4/MDR3 Sequencing
>> Mitochondrial DNA Analysis

ABCB11 Sequencing
>> Mitochondrial DNA Analysis

ACADL Sequencing
>> Mitochondrial DNA Analysis

ACADVL Sequencing
>> Mitochondrial DNA Analysis

Adenine Nucleotide Translocase 1 (ANT1/ SLC25A4) Sequencing
>> Mitochondrial DNA Analysis

Aldolase B Deficiency
>> Mitochondrial DNA Analysis

Alpers Syndrome
>> Mitochondrial DNA Analysis

Arginase
>> Biochemical Analysis
>> ARG1 Sequencing

ATPase Subunits
>> Mitochondrial DNA Analysis

ATP8B1 Sequencing
>> Mitochondrial DNA Analysis

Autosomal Dominant Progressive External Ophthalmoplegia (ad-PEO)
>> Panel (includes POLG1, TWINKLE, & ANT1)
>> Adenine Nucleotide Translocase 1 (ANT1/SLC25A4) Sequencing
>> TWINKLE/PEO1 Sequencing

Autosomal Dominant Progressive External Ophthalmoplegia (ad-PEO) with mtDNA Deletions-4 (PEOA4)
>> Mitochondrial DNA Analysis

B

BCS1L Sequencing
>> Mitochondrial DNA Analysis

Benign Recurrent Intrahepatic Cholestasis 1 (BRIC1)
>> Mitochondrial DNA Analysis

Benign Recurrent Intrahepatic Cholestasis 2 (BRIC2)
>> Mitochondrial DNA Analysis

Bile Salt Excretory Pump Disease (BSEP)
>> Mitochondrial DNA Analysis

Biotinidase
>> Biochemical Analysis
>> BTD Sequencing

Byler Disease
>> Mitochondrial DNA Analysis

 

C

CACT Deficiency
>> Mitochondrial DNA Analysis

Carbamoyl Phosphate Synthetase I Deficiency - CPS1 Sequencing
>> Mitochondrial DNA Analysis

Carnitine-Acylcarnitine Translocase Deficiency
>> Mitochondrial DNA Analysis

Carnitine Palmitoyltransferase 1 Deficiency - CPT1A Sequencing
>> Mitochondrial DNA Analysis

Carnitine Palmitoyltransferase 1 Deficiency - CPT1B Sequencing
>> Mitochondrial DNA Analysis

Carnitine Palmitoyltransferase II Deficiency - CPT2 Sequencing
>> Mitochondrial DNA Analysis

Carnitine Transporter Deficiency
>> Mitochondrial DNA Analysis

Carotid Body Tumors and Multiple Extraadrenal Pheochromocytomas
>> Succinate Dehydrogenase Complex Subunit B (SDHB) Sequencing
>> Succinate Dehydrogenase Complex Subunit D (SDHD) Sequencing

Citrin Deficiency
>> Mitochondrial DNA Analysis

Citrullinemia Type II (CTLN2)
>> Mitochondrial DNA Analysis

Coenzyme Q10 Deficiency
>> COQ2 Sequencing
>> PDSS1 Sequencing
>> PDSS2 Sequencing

Complex I Subunits
>> Mitochondrial DNA Analysis

Complex I Deficiency
>> C6ORF66 Sequencing
>> NDUFA1 Sequencing

Complex III Deficiency (BCS1L Related)
>> Mitochondrial DNA Analysis

Complex IV (COX) Deficiency
>> SURF1, SCO2, SCO1, and COX10 Sequencing

COX10 Sequencing
>> Mitochondrial DNA Analysis

Creatine Transporter (CRTR) Deficiency -
CT1/SLC6A8 Sequencing
>> Mitochondrial DNA Analysis

Cytochrome b Subunit
>> Mitochondrial DNA Analysis

Cytochrome c Oxidase (COX) Subunits
>> Mitochondrial DNA Analysis

 

D

Deafness-Dystonia-Optic Neuropathy Syndrome (DDP1)
>> Mitochondrial DNA Analysis

Deoxyguanosine Kinase (DGUOK) Sequencing
>> Mitochondrial DNA Analysis

Dihydrolipoyl dehydrogenase (E3) Deficiency - DLD Sequencing
>> Mitochondrial DNA Analysis

 

E

Electron Transport Chain Enzymes
>> Mitochondrial DNA Analysis

Encephalomyopathic Mitochondrial DNA Depletion Syndrome
>> SUCLA2 Sequencing

 

F

FAH Sequencing
>> Mitochondrial DNA Analysis

Familial Nonchromaffin Paragangliomas
>> Succinate Dehydrogenase Complex Subunit B (SDHB) Sequencing
>> Succinate Dehydrogenase Complex Subunit C (SDHC) Sequencing
>> Succinate Dehydrogenase Complex Subunit D (SDHD) Sequencing

Fatal Infantile Lactic Acidosis with mtDNA Depletion - SUCLG1 Sequencing
>> Mitochondrial Analysis

G

GATM Sequencing
>> Mitochondrial DNA Analysis

Glycogen Storage Disease Type 1A (GSD1A) - G6PC Sequencing
>> Mitochondrial DNA Analysis

Glycogen storage disease type 0 (GSD0) - GYS2 Sequencing
>> Mitochondrial DNA Analysis

Guanidinoacetate Methyltransferase (GAMT) - GAMT Sequencing
>> Mitochondrial DNA Analysis

 

H

Hepatocerebral mtDNA Depletion Panel - POLG1, DGUOK & MPV17 Sequencing
>> Mitochondrial DNA Analysis

Hereditary Fructose Intolerance - ALDOB Sequencing
>> Mitochondrial DNA Analysis

Holocarboxylase Deficiency - HLCS Sequencing
>> Mitochondrial DNA Analysis

 

I

Infantile Hepatic Mitochondrial DNA Depletion - MPV17 Sequencing
>> Mitochondrial DNA Analysis

 

K

Kearns-Sayre Syndrome
>> Mitochondrial DNA Deletion Analysis

 

L

L-Arginine:Glycine Amidinotransferase Deficiency - GATM Sequencing
>> Mitochondrial DNA Analysis

Leber's Optic Neuropathy (LON) Point Mutations
>> Mitochondrial DNA Analysis

Leigh Syndrome
>> Mitochondrial DNA Analysis

Liver Glycogen Synthase Deficiency
>> Mitochondrial DNA Analysis

Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD)
>> Mitochondrial DNA Analysis

Very Long Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD)
>> Mitochondrial DNA Analysis

Long Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
>> Mitochondrial DNA Analysis

 

M

Maple Syrup Urine Disease Type 3 - DLD Sequencing
>> Mitochondrial DNA Analysis

Maternally Inherited Sensorineural Hearing Loss (MISNHL)
>> Mitochondrial DNA Analysis

MDR3 Disease
>> Mitochondrial DNA Analysis

Medium Chain acyl-CoA Dehydrogenase Deficiency (MCAD)
>> Mitochondrial DNA Analysis

Methylmalonic Aciduria and Homocystinuria, cblC Type
>> Mitochondrial DNA Analysis

Mitochondrial DNA (mtDNA) Content (qPCR) Analysis
>> Mitochondrial DNA Analysis

Mitochondrial DNA Deletion Syndrome
>> Mitochondrial DNA Deletion Analysis

Mitochondrial DNA Depletion and Multiple Deletions - POLG1, TK2, SUCLA2 & DGUOK Sequencing
>> Mitochondrial DNA Analysis

Mitochondrial DNA Screening Panel (Point Mutations and Deletions)
>> Mitochondrial DNA Analysis

Mitochondrial DNA Screen Panel Quantification
>> Mitochondrial DNA Analysis

Mitochondrial Encephalomyopathy, Lactic Acidosis, and Stroke-Like Episodes (MELAS)
>> Mitochondrial DNA Analysis

MitoMetSM Mitochondrial/Metabolic oligonucleotide array CGH analysis
>> Mitochondrial DNA Analysis

Mitochondrial Phosphate Carrier Deficiency - SLC25A3 (PHC) Sequencing
>> Mitochondrial DNA Analysis

Mitochondrial Respiratory Chain Complex II Deficiency
>> Succinate Dehydrogenase Complex Subunit A (SDHA) Sequencing
>> Succinate Dehydrogenase Complex Subunit B (SDHB) Sequencing
>> Succinate Dehydrogenase Complex Subunit C (SDHC) Sequencing
>> Succinate Dehydrogenase Complex Subunit D (SDHD) Sequencing

Mitochondrial Respiratory Chain Enzymes
>> Mitochondrial DNA Analysis

MMACHC Sequencing
>> Mitochondrial DNA Analysis

MNGIE Syndrome
>> Biochemical Analysis
>> Mitochondrial DNA Analysis

Mohr-Tranebjaerg syndrome
>> Mitochondrial DNA Analysis

MPV17 Sequencing
>> Mitochondrial DNA Analysis

Myoclonic Epilepsy Associated with Ragged-Red Fibers (MERRF)
>> Mitochondrial DNA Analysis

Myopathic Mitochondrial DNA Depletion Syndrome
>> TK2 Sequencing
>> RRM2B Sequencing

 

N

N-Acetylglutamate Synthase Deficiency - NAGS Sequencing
>> Mitochondrial DNA Analysis

NADH-ubiquinone oxidoreductase 1 alpha subcomplex 1 - NDUFA1 Sequencing
>> Mitochondrial DNA Analysis

NADH-ubiquinone oxidoreductase Fe-S Protein 4 Sequence Analysis - NDUFS4 Sequencing
>> Mitochondrial DNA Analysis

NADH-ubiquinone oxidoreductase 1 alpha assembly factor 2 Sequence Analysis - NDUFAF2/NDUFA12L Sequencing
>> Mitochondrial DNA Analysis

Neuropathy, Ataxia, and Retinitis Pigmentosa (NARP) and Mitochondrial DNA Associated Leigh Syndrome
>> Mitochondrial DNA Analysis

 

O

Optic Atrophy Type I - OPA1 Sequencing
>> Mitochondrial DNA Analysis


Organic Cation Transporter (OCTN2) Sequencing

>> Mitochondrial DNA Analysis

Ornithine Transcarbamylase (OTC) Deficiency
>> Biochemical Analysis
>> Mitochondrial DNA Analysis

 

P

PDSS1 Sequencing
>> Mitochondrial DNA Analysis

PDSS2 Sequencing
>> Mitochondrial DNA Analysis

Pearson Syndrome
>> Mitochondrial DNA Deletion Analysis

Phenylketonuria (PKU)
>> Biochemical Analysis
>> Mitochondrial DNA Analysis

Pheochromocytoma (PHEO) and Paraganglioma (PGL)-Associated Syndromes Panel
>> Succinate Dehydrogenase Complex Subunit B (SDHB) Sequencing
>> Succinate Dehydrogenase Complex Subunit C (SDHC) Sequencing
>> Succinate Dehydrogenase Complex Subunit D (SDHD) Sequencing

POLG1 Related Disorders - POLG1 Sequencing
>> Mitochondrial DNA Analysis

POLG2 Sequencing
>> Mitochondrial DNA Analysis

Progressive Familial Intrahepatic Cholestasis 1 (PFIC1)
>> Mitochondrial DNA Analysis

Progressive Familial Intrahepatic Cholestasis 2 (PFIC2)
>> Mitochondrial DNA Analysis

Progressive Familial Intrahepatic Cholestasis 3 (PFIC3)
>> Mitochondrial DNA Analysis

Pyruvate Dehydrogenase Deficiency - PDHA1 Sequencing
>> Mitochondrial DNA Analysis

R

RRM2B Sequencing
>> Mitochondrial DNA Analysis

S

SCO1 Sequencing
>> Mitochondrial DNA Analysis

SCO2 Sequencing
>> Mitochondrial DNA Analysis

SLC25A3 (PHC) Sequencing
>> Mitochondrial DNA Analysis

SLC25A13 Sequencing
>> Mitochondrial DNA Analysis

SLC25A20 Sequencing
>> Mitochondrial DNA Analysis

SUCLA2 Sequencing
>> Mitochondrial DNA Analysis

SUCLG1 Sequencing
>> Mitochondrial Analysis

Succinate Dehydrogenase Complex Subunit A (SDHA) Sequencing
>> Mitochondrial DNA Analysis

Succinate Dehydrogenase Complex Subunit B (SDHB) Sequencing
>> Mitochondrial DNA Analysis

Succinate Dehydrogenase Complex Subunit C (SDHC) Sequencing
>> Mitochondrial DNA Analysis

Succinate Dehydrogenase Complex Subunit D (SDHD) Sequencing
>> Mitochondrial DNA Analysis

SURF1 Sequencing
>> Mitochondrial DNA Analysis

Systemic Carnitine Deficiency - SLC22A5 Sequencing
>> Mitochondrial DNA Analysis

 

T

TIMM8A Sequencing
>> Mitochondrial DNA Analysis

Thymidine Kinase (TK2) Sequencing
>> Mitochondrial DNA Analysis

Thymidine Phosphorylase (TP), TYMP Sequencing
>> Mitochondrial DNA Analysis

TOMM20 Sequencing
>> Mitochondrial DNA Analysis

TWINKLE/PEO1 Sequencing
>> Mitochondrial DNA Analysis

Tyrosinemia Type 1
>> Mitochondrial DNA Analysis

 

W

Whole Genome
>> Mitochondrial DNA Analysis